MAPCAs are abnormal congenital blood vessels that originate from the aorta or one of its first-order branches and connect with the pulmonary arteries. They frequently occur in patients with complex congenital heart disease, including pulmonary atresia and Tetralogy of Fallot.
Because a specific ICD-10-CM code does not identify MAPCAs by name, coders must determine which congenital malformation category best represents the condition.
Coding Clinic directs assignment of:
Q28.8 — Other specified congenital malformations of circulatory system
The diagnosis should not be coded as an acquired vascular disorder simply because the MAPCA is evaluated or treated later in the patient’s life. The vessel remains a congenital malformation.
Let’s now consider a patient with a history of multiple congenital heart conditions including; Tetralogy of Fallot, MAPCAs, pulmonary artery unifocalization, ventricular septal defect, pulmonary atresia, and placement of a right ventricle-to-pulmonary artery conduit.
During cardiac catheterization, angiography demonstrates collateral blood flow involving several vessels and the right lung. A microcatheter is advanced into an aortopulmonary collateral arising from the descending aorta. A microvascular plug and coils are deployed to occlude the collateral vessel. Follow-up angiography confirms that flow has been reduced to a minimal level.
Coding Clinic directs assignment of:
02LQ3DZ — Occlusion of right pulmonary artery with intraluminal device, percutaneous approach
Elements that support this code:
- Root operation: Occlusion, because the objective is to completely close the collateral vessel.
- Body part: Right pulmonary artery, which adequately represents the treated site.
- Approach: Percutaneous, based on catheter access.
- Device: Intraluminal device, representing the coils and vascular plug left within the vessel.
The operative report should clearly identify:
- The vessel being treated
- The origin and destination of the collateral
- The side involved
- The objective of the embolization
- The type of device deployed
- The catheter-based approach
- The post-embolization blood-flow findings
Organizations should incorporate this guidance into congenital cardiac coding education, encoder notes, and procedure-audit tools. When the anatomy is complex, collaboration among the coder, clinical documentation integrity specialist, and physician may be necessary to ensure that the coded body part accurately represents the procedure.
About the Author
Dianna Foley, RHIA, CCS, CDIP, CHPS, has 25 years of HIM experience. She earned her bachelor’s degree from the University of Cincinnati and holds RHIA, CHPS, CDIP, and CCS certifications from AHIMA. Dianna’s an AHIMA-approved ICD-10-CM/PCS trainer, an AHIMA-published author, a participant in AHIMA credential item writing and exam development, and served on the AHIMA Nominating Committee. Dianna has held various HIM positions and is now an independent coding consultant. She previously served as a program director for Medical Coding and HIT. She presents on coding topics at the national, state, and regional levels and serves as OHIMA’s Education Coordinator.




